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Case Report
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| Non-syndromic multiple keratocystic odontogenic tumors: An arduous challenge for oral and maxillofacial specialists | ||||||
| GV Reddy1, M Haranadha Reddy2, Garlapati Komali3, Rembers Anusha4, Pancha Venkat Bhagirath5, Raj Kumar Badam6, K. Sravan Kumar Reddy7 | ||||||
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1MDS, Professor & Head of the Department, Oral and maxillofacial Surgery, Panineeya Mahavidyalaya Institute of Dental Sciences and Research Centre, Hyderabad,Telangana, India.
2MDS, Professor, Oral and Maxillofacial Surgery, Panineeya Mahavidyalaya Institute of Dental Sciences and Research Centre, Hyderabad, Telangana, India. 3MDS, Professor, Oral Medicine and Radiology, Panineeya Mahavidyalaya Institute of Dental Sciences and Research Centre, Hyderabad, Telangana, India. 4BDS, Post Graduate Student, Oral Medicine and Radiology, Panineeya Mahavidyalaya Institute of Dental Sciences and Research Centre, Hyderabad, Telangana, India. 5MDS, Professor & Head of the Department, Oral and Maxillofacial Pathology, Panineeya Mahavidyalaya Institute of Dental Sciences and Research Centre, Hyderabad, Telangana, India. 6MDS, Reader, Oral Medicine and Radiology, Panineeya Mahavidyalaya Institute of Dental Sciences and Research Centre, Hyderabad, Telangana, India. 7BDS, Post Graduate Student, Oral and Maxillofacial Surgery, Panineeya Mahavidyalaya Institute of Dental Sciences and Research Centre, Hyderabad,Telangana, India. | ||||||
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| How to cite this article |
| Reddy GV, Reddy MH, Garlapati K, Garlapati K, Bhagirath PV, RK Badam, Reddy KSK. Non-syndromic multiple keratocystic odontogenic tumors: An arduous challenge for oral and maxillofacial specialists. Int J Case Rep Images 2016;7(6):360–364. |
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Abstract
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Introduction:
Keratocystic odontogenic tumor (KOT) is a common developmental odontogenic cyst affecting the maxillofacial region. Multiple odontogenic keratocysts (OKCs) are usually seen in association with nevoid basal cell carcinoma syndrome but approximately only 5% of patients with keratocystic odontogenic tumor have multiple cysts without concomitant syndromic presentation. Only a few cases have been reported till date.
Case Report: This report emphasizes a unique case of a young 14-year-old female suffering since an early age and the role of multidisciplinary approach in the diagnosis and management of a case of multiple keratocystic odontogenic tumors in a non-syndromic patient. Conclusion: The non-syndromic KCOTs are linked to the expression of a characteristic gene. They are associated with severe morbidity in the younger age group due to their multiple involvement of the jaws but their recurrence rate is less compared to that of syndromic type. The diagnosis and management of these tumors mandates multidisciplinary approach which can instill confidence and improve quality of life of the patients. | |
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Keywords:
Keratocystic odontogenic tumor, Benign neoplasm, Gorlin –Goltz syndrome, Tumor suppressor gene
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Author Contributions
GV Reddy – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Haranadha Reddy M. – Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Komali Garlapati – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Anusha Rembers – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Venkat Bhagirath Pancha – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Raj Kumar Badam – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published K. Sravan Kumar Reddy – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published. |
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Guarantor of submission
The corresponding author is the guarantor of submission. |
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Source of support
None |
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Conflict of interest
Authors declare no conflict of interest. |
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Copyright
© 2016 GV Reddy et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information. |
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