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Case Report
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| Retroperitoneal desmoid tumor with unusual appearance as a spontaneous ureteral rupture and rare association with desmoid tumor of the breast | ||||||
| Faouzi Mallat1, Wissem Hmida1, Sarra Mestiri2, Badreddine Sriha2, Moncef Mokni2, Faouzi Mosbah1 | ||||||
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1Urology Department, Sahloul Hospital, Sousse.
2Pathology Department, Fahat Hached Hospital, Sousse. | ||||||
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| Mallat F, Hmida W, Mestiri S, Sriha B, Mokni M, Mosbah F. Retroperitoneal desmoid tumor with unusual appearance as a spontaneous ureteral rupture and rare association with desmoid tumor of the breast. International Journal of Case Reports and Images 2014;5(5):38–42. |
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Abstract
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Introduction:
Desmoid tumors of retroperitoneum and breast are rare. Their association is exceptional and their management is controversial. Spontaneous ureteral rupture as a complication and a circumstance of discovery of the retroperitoneal desmoid tumor is a rare entity and poses management difficulties. To the best of our knowledge, this case is the first to present this exceptional association, and to report the ureteral rupture as a circumstance of discovery of the retroperitoneal desmoid tumor.
Case Report: We present the first reported case, seen in a young girl without Gardner's syndrome, in which upper ureteral rupture was the primary symptom of an aggressive retroperitoneal desmoid tumor. She underwent laparotomy for septic peritonitis secondary to rupture of the right ureter, in which initially right ureterocutaneostomy was done, later right nephrectomy was made; for recurrent right ureteral rupture. Imatinib (Glivec) 200 mg was prescribed. However, due to intractable diarrhea, the target therapy was discontinued. At follow-up, left breast desmoid tumor was diagnosed by mammography, sonography and magnetic resonance imaging scan; and confirmed by sonographically guided core biopsy; and large excision was made. At the last follow-up, radiological exams did not show any significant change in size of the retroperitoneal masse or recurrent tumor in the breast or other sites. Conclusion: Desmoid tumors can occur synchronously or metachronously in many locations, even the absence of Gardner's syndrome. Their evolution is unpredictable and it may be complicated, in the case of retroperitoneal desmoid tumor, by spontaneous ureteral rupture that should be considered. | |
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Keywords:
Retroperitoneal desmoid tumor, Spontaneous ureteral rupture, Breast desmoid tumor
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Author Contributions
Faouzi Mallat – Substantial contributions to conception and design, Acquisition of data, Drafting the article, Revising it critically for important intellrctual content, Final approval of the version to be published Wissem Hmida – Substantial contributions to conception and design, Acquisition of data, Drafting the article, Revising it critically for important intellrctual content, Final approval of the version to be published Sarra Mestiri – Substantial contributions to conception and design, Acquisition of data, Drafting the article, Final approval of the version to be published Badreddine Sriha – Substantial contributions to conception and design, Drafting the article, revising it critically for important intellrctual content, Final approval of the version to be published Moncef Mokni – Substantial contributions to conception and design, Drafting the article, Final approval of the version to be published Faouzi Mosbah – Substantial contributions to conception and design, Acquisition of data, Drafting the article, revising it critically for important intellrctual content, Final approval of the version to be published |
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Guarantor of submission
The corresponding author is the guarantor of submission. |
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Source of support
None |
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Conflict of interest
Authors declare no conflict of interest. |
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Copyright
© 2014 Faouzi Mallat et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information. |
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