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Case Report
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| Primary leiomyosarcoma of the nipple-areola complex with an unusual clinical presentation: A case report | ||||||
| Xavier Guedes1, Meritxell Medarde2, Tamara Parra3, MJ Martinez3, Enric de Caralt4, Constanti Serra5 | ||||||
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1MD, Member of Staff of the Department of General Surgery, Consorci Hospitalari de Vic, Barcelona, Spain.
2MD, Member of Staff of the Department of General Surgery and Breast Surgery, Consorci Hospitalari de Vic, Barcelona, Spain. 3MD, Member of Staff of the Department of Pathology, Consorci Hospitalari de Vic, Barcelona, Spain. 4MD, Chief of Staff of the Department of General Surgery, Consorci Hospitalari de Vic, Barcelona, Spain. 3MD, Member of Staff of the Department of General Surgery and Chief of Breast Surgery Consorci Hospitalari de Vic, Barcelona, Spain. | ||||||
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| How to cite this article: |
| Guedes X, Medarde M, Parra T, Martinez MJ, de Caralt E, Serra C. Primary leiomyosarcoma of the nipple-areola complex with an unusual clinical presentation: A case report. International Journal of Case Reports and Images 2014;5(1):66–70. |
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Abstract
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Introduction:
Primary leiomyosarcoma of the nipple is a rare disease that accounts for less than 0.1% of all malignant tumors of the breast. About 35 cases have been described in English literature.
Case Report: We report a case of a 46-year-old female presenting with a two-year suppurative squamous plaque-type lesion of the right nipple at first considered as an unusual Paget’s disease presentation. No adenopathies or associated lesions were identified. Core biopsy was informed as a possible leiomyosarcoma. It was decided to remove the lesion surgically by wide excision of the nipple-areola complex with adequate surgical margins with no lymph node dissection or adjuvant radiochemotherapy. Histopathology and immunohistochemistry confirmed the diagnosis of leiomyosarcoma. One year after the surgery there are no recurrences or distant metastasis. Conclusion: More data and long-term follow-up is necessary to understand prognosis and develop an adequate treatment protocol for this type of neoplasms. | |
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Keywords:
Leiomyosarcoma, Breast, Sarcoma, Nipple-areola complex
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Author Contributions
Xavier Guedes – Substantial contributions to conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published Meritxell Medarde – Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published Tamara Parra – Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published MJ Martinez – Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published Enric de Caralt – Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published Constanti Serra – Substantial contributions to conception and design, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published |
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Guarantor of submission
The corresponding author is the guarantor of submission. |
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Source of support
None |
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Conflict of interest
Authors declare no conflict of interest. |
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Copyright
© Xavier Guedes et al. 2014; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.) |
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