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Case Report
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| Mid-aortic dysplastic syndrome as a rare cause of hypertension in young | ||||||
| Kaushik Saha1, Dipa Saha2, Parinita Ranjit3, Sujoy Sarkar3, Rabi Ranjan Sow Mondal4, Thiyagrajan G4 | ||||||
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1MBBS, DCH, MD (Medicine), Assistant Professor, Department of General Medicine, Calcutta National Medical College, Kolkata.
2MBBS, MD (Physiology), Assistant Professor, Department of Physiology, College of Medicine & JNM Hospital, Kalyani, West Bengal. 3MBBS, MD (PGT), 3rd year post graduate trainee, Department of General Medicine, Calcutta National Medical College, Kolkata. 4MBBS, MD (PGT), 2nd year post graduate trainee, Department of General Medicine, Calcutta National Medical College, Kolkata. | ||||||
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| How to cite this article: |
| Saha K, Saha D, Ranjit P, Sarkar S, Mondal RRS, Thiyagrajan G. Mid aortic dysplastic syndrome as a rare cause of hypertension in young. International Journal of Case Reports and Images 2013;4(10):563–566. |
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Abstract
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Introduction:
Mid-aortic syndrome (MAS), coarctation of abdominal aorta is a rare disease with only 200 reported cases. It is characterized by constriction of distal thoracic and/or abdominal aorta and its branches, therefore is also known as abdominal aortic coarctation. The MAS is characterized radiologically by severe narrowing of abdominal aorta and its branches and most of these patients usually die due to progressive severe hypertension before the age of 35–40 if left untreated.
Case Report: A 13-year-old boy was admitted with persistent headache and vomiting for one month and repeated generalized tonic clonic seizures for two days. His past history was unremarkable. The highlight of the clinical examination blood pressure was 240/150 mmHg in both the upper limbs, and all peripheral pulses were palpable. Blood pressure was similar in upper and lower limbs and a systolic bruit heard over the epigastrium. Ultrasonography showed a localized narrowing of a suprarenal segment of the abdominal aorta with an abrupt focal dilatation of the abdominal aorta approx 1.7 cm below origin of superior mesenteric artery. Magnetic resonance angiography of the aorta and its branches showed a distinct fusiform dilatation of abdominal aorta just below the origin of the superior mesenteric artery. Focal narrowing of abdominal aorta was noted just proximal to the dilatation. Conclusion: We diagnosed a case of mid-aortic coarctation with post stenotic dilatation associated with left renal artery stenosis leading to secondary hypertension in a teenage boy presenting with reversible posterior leukoencephalopathy and seizures. The boy was referred for vascular surgery but the patient refused any operative procedure. | |
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Keywords:
Mid-aortic dysplastic syndrome (MAS), Secondary hypertension, Posterior leukoencephalopathy
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Author Contributions
Kaushik Saha – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Dipa Saha – Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Parinita Ranjit – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Sujoy Sarkar – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Rabi Ranjan Sow Mondal – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Final approval of the version to be published Thiyagrajan G – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published |
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Guarantor of submission
The corresponding author is the guarantor of submission. |
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Source of support
None |
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Conflict of interest
Authors declare no conflict of interest. |
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Copyright
© Kaushik Saha et al. 2013; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.) |
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