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Case Series
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| Papillon Lefevre syndrome: A periodontist approach |
| Jayachandran Dorairaj1, Sunantha Selvaraj2, Mohammed Sadique2, Michael Shaw3, Sachin Kumar Amruthlal Jain3 |
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1Department of periodontics, Vinayaka Missions Sankarachariyar Dental College, Salem, Tamilnadu, India.
2Department of Prosthodontics, Vinayaka Missions Sankarachariyar Dental College, Salem, Tamilnadu, India. 3Department of Internal Medicine, Providence Hospital and Medical Centers, Southfield, MI, USA. |
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doi:10.5348/ijcri-2012-07-140-CS-1
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Address correspondence to: Sachin Kumar Amruthlal Jain, MD Department of Internal Medicine, Providence Hospital and Medical Centers 16001 W. Nine Mile Road Southfield, MI 48075 USA Phone: 248 849 3968 Fax: 248 849 3151 Email: doctorsachin@gmail.com |
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| How to cite this article: |
| Dorairaj J, Selvaraj S, Sadique M, Shaw M, Jain SKA. Papillon Lefevre syndrome: A periodontist approach. International Journal of Case Reports and Images 2012;3(7):1–5. |
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Abstract
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Introduction:
Papillon-Lefevre Syndrome (PLS) is a rare autosomal recessive disorder of keratinisation, characterized by palmoplantar hyperkeratosis, periodontitis and early loss of dentition. Since these features are common to both dentistry and dermatology, members of both disciplines should be aware of the same because an early diagnosis of this condition can help to preserve the teeth by early institution of treatment, using a multidisciplinary approach.
Case Series: The authors here present two cases of Papillon-Lefevre syndrome in siblings, having all of the characteristic features, along with a comprehensive review of the etiology, pathology, clinical features, differential diagnosis and management of the condition. Conclusion: The main priority of physician's strategy is to refer the PLS patients at the earliest to a periodontist for the periodontal management of permanent dentition. Based on the previously reported series and our clinical experience, non-surgical periodontal therapy yielded better results when started immediately after the extraction of deciduous dentition. | |
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Key Words:
Palmoplantar hyperkeratosis, Papillon Lefevre syndrome, Periodontitis
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Author Contributions:
Jayachandran Dorairaj - Substantial contributions to conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article or revising it critically for important intellectual content, Final approval of the version to be published Sunantha Selvaraj - Substantial contributions to conception and design and interpretation of data, Drafting the article, Final approval of the version to be published Mohammed Sadique - Substantial contributions to conception, and analysis, Drafting the article or revising it critically for important intellectual content, Final approval of the version to be published Michael Shaw - Substantial contributions to design and interpretation of data, Drafting the article or revising it critically for important intellectual content, Final approval of the version to be published Sachin Kumar Amruthlal Jain - Substantial contributions to interpretation of data, Drafting the article or revising it critically for important intellectual content, Final approval of the version to be published |
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Guarantor of submission:
The corresponding author is the guarantor of submission. |
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Source of support:
None |
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Conflict of interest:
Authors declare no conflict of interest. |
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Copyright:
© Jayachandran Dorairaj et al. 2012; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.) |
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