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Case Report
1 MD, Obstetric Unit, Evangelico Betania Hospital, Naples, Italy
2 MD, Pediatric Cardiology Unit, Monaldi Hospital, Campania University “Luigi Vanvitelli”, Monaldi Hospital, Naples, Italy
3 MD, Cardiothoracic Surgery Unit, Monaldi Hospital, Naples, Italy
4 MD, Head of Department, Cardiothoracic Surgery Unit, Monaldi Hospital, Naples, Italy
5 MD, Head of Department, Pediatric Cardiology Unit, Monaldi Hospital, Campania University “Luigi Vanvitelli”, Naples, Italy
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Beniamino Tormettino
Corso Vittorio Emanuele 211, Naples,
Italy
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Article ID: 100072Z08BT2021
Introduction: Vascular rings are congenital anomalies of the aortic arch system characterized by a vascular anomalies of mediastinal vessels that encircle and compress the esophagus and trachea. Aortic arch anomalies may be associated with other congenital cardiac defects or chromosomal anomalies, such as microdeletion of chromosome 22q11. In neonatal/pediatric life, clinical presentation shows stridor and difficulty in swallowing or dysphagia.
Case Report: We describe a particular case diagnosed in fetal life with a symptomatic vascular ring in neonatal life: left circumflex retroesophageal aortic arch, right patent ductus arteriosus “PDA”/ligamentum arteriosum, and aberrant right subclavian artery “ARSA.”
Conclusion: To the best of our knowledge, we described a novel vascular ring diagnosed in fetal life and symptomatic in neonatal life. In this extremely rare case, a “true” vascular ring, like in case of double aortic arch, it is due by the left circumflex retroesophageal aortic arch, ARSA, and right patent ductus/ligamentum arteriosum.
Keywords: Aberrant right subclavian artery, Circumflex retroesophageal aortic arch, Three vessel and trachea view, Vascular ring
Thanks to M Giodano and L Di Pietto L who contributed to the work but do not qualify for authorship.
Author ContributionsBeniamino Tormettino - Substantial contributions to conception and design, Analysis of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Carmela Morelli - Substantial contributions to conception and design, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published
Andrea Serrao - Acquisition of data, Analysis of data, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published
Guido Oppido - Acquisition of data, Analysis of data, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published
Maria Giovanna Russo - Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published
Guarantor of SubmissionThe corresponding author is the guarantor of submission.
Source of SupportNone
Consent StatementWritten informed consent was obtained from the patient for publication of this article.
Data AvailabilityAll relevant data are within the paper and its Supporting Information files.
Conflict of InterestAuthors declare no conflict of interest.
Copyright© 2021 Beniamino Tormettino et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.