Case Report


A novel symptomatic vascular ring in a neonate

,  ,  ,  ,  

1 MD, Obstetric Unit, Evangelico Betania Hospital, Naples, Italy

2 MD, Pediatric Cardiology Unit, Monaldi Hospital, Campania University “Luigi Vanvitelli”, Monaldi Hospital, Naples, Italy

3 MD, Cardiothoracic Surgery Unit, Monaldi Hospital, Naples, Italy

4 MD, Head of Department, Cardiothoracic Surgery Unit, Monaldi Hospital, Naples, Italy

5 MD, Head of Department, Pediatric Cardiology Unit, Monaldi Hospital, Campania University “Luigi Vanvitelli”, Naples, Italy

Address correspondence to:

Beniamino Tormettino

Corso Vittorio Emanuele 211, Naples,

Italy

Message to Corresponding Author


Article ID: 100072Z08BT2021

doi: 10.5348/100072Z08BT2021CR

Access full text article on other devices

Access PDF of article on other devices

How to cite this article

Tormettino B, Morelli C, Serrao A, Oppido G, Russo MG. A novel symptomatic vascular ring in a neonate. J Case Rep Images Obstet Gynecol 2021;7: 100072Z08BT2021.

ABSTRACT


Introduction: Vascular rings are congenital anomalies of the aortic arch system characterized by a vascular anomalies of mediastinal vessels that encircle and compress the esophagus and trachea. Aortic arch anomalies may be associated with other congenital cardiac defects or chromosomal anomalies, such as microdeletion of chromosome 22q11. In neonatal/pediatric life, clinical presentation shows stridor and difficulty in swallowing or dysphagia.

Case Report: We describe a particular case diagnosed in fetal life with a symptomatic vascular ring in neonatal life: left circumflex retroesophageal aortic arch, right patent ductus arteriosus “PDA”/ligamentum arteriosum, and aberrant right subclavian artery “ARSA.”

Conclusion: To the best of our knowledge, we described a novel vascular ring diagnosed in fetal life and symptomatic in neonatal life. In this extremely rare case, a “true” vascular ring, like in case of double aortic arch, it is due by the left circumflex retroesophageal aortic arch, ARSA, and right patent ductus/ligamentum arteriosum.

Keywords: Aberrant right subclavian artery, Circumflex retroesophageal aortic arch, Three vessel and trachea view, Vascular ring

SUPPORTING INFORMATION


Acknowledgments

Thanks to M Giodano and L Di Pietto L who contributed to the work but do not qualify for authorship.

Author Contributions

Beniamino Tormettino - Substantial contributions to conception and design, Analysis of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published

Carmela Morelli - Substantial contributions to conception and design, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published

Andrea Serrao - Acquisition of data, Analysis of data, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published

Guido Oppido - Acquisition of data, Analysis of data, Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published

Maria Giovanna Russo - Interpretation of data, Revising it critically for important intellectual content, Final approval of the version to be published

Guarantor of Submission

The corresponding author is the guarantor of submission.

Source of Support

None

Consent Statement

Written informed consent was obtained from the patient for publication of this article.

Data Availability

All relevant data are within the paper and its Supporting Information files.

Conflict of Interest

Authors declare no conflict of interest.

Copyright

© 2021 Beniamino Tormettino et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.