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Case Report
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| Malignant triton tumor of maxilla: A case report | ||||||
| Rajjyoti Das1, Anupam Sarma2, Partha Sarathi Chakraborty3, Jagannath Dev Sharma4, Amal Chandra Kataki5 | ||||||
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1MBBS, MS,Assistant Professor, Department of Head & Neck Oncology, Dr. B. Borooah Cancer Institute. Guwahati, Assam, India.
2MBBS, MD, Assistant Professor, Department of Pathology, Dr. B. Borooah Cancer Institute, Guwahati , Assam, India. 3BDS, MDS, P.G. Fellow, Department of Head & Neck Oncology, Dr. B. Borooah Cancer Institute, Guwahati, Assam, India. 4MBBS, MD,Professor& Head, Department of Pathology, Dr. B. Borooah Cancer Institute, Guwahati, Assam, India. 5MBBS, MD,Director& Head, Department of Gynaecologic Oncology, Dr. B. Borooah Cancer Institute. Guwahati, Assam, India. | ||||||
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| How to cite this article |
| Das R, Sarma A, Chakraborty P. Malignant triton tumor of maxilla: A case report. International Journal of Case Reports and Images 2014;5(2):160–164. |
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Abstract
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Introduction:
Malignant triton tumor (or malignant Schwanoma with Rhabdomyoblastic differentiation) is a very rare entity with poor prognosis. It isconsidered a high grade malignantneoplasm with poor outcome. In 70% of cases the neoplasm is associated with von Recklinghausen neurofibromatosis and in the remaining 30% it is the sole morbid finding. Local recurrence is frequent and distant metastasis preferentially situated in lung and brain. Surgery is the treatment of choice and post operative radiotherapy is always indicated. Histopathology and immunohistochemistry are helpful in diagnosis. We report clinical course, therapeutic approach, histopathology and immunohistochemistry of such a case.
Case Report: A 19-year-old female presented in Dr B Borooah Cancer Institute, Guwahati with a complaint of swelling in the right side of the cheek with ulceration in the oral cavity. On clinical examination there was a round swelling in left cheek of 4x4 cm size with overlying normal skin. Computed tomography scan revealed a hypo dense lesion in the right maxillary sinus with erosion of the floor. Punch biopsy was taken from palatal growth and sent for histopathological examination which revealed a malignant neoplasm with sarcomatoid features composed of spindle cells. Immunohistochemical stains showed tumor cells positive for Vimentin, S-100 protein and, Desmin. Patient was taken up for surgery followed by radiotherapy. Conclusion: Malignant triton tumor of maxilla is extremely rare. The diagnosis must be based upon imaging study, histopathology and immunohistochemical features. Considering the aggressive nature of disease radical surgery should be followed by adjuvant chemoradiation. | |
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Keywords:
Malignant triton tumor (MTT), Surgery, Histopathology and immunohistochemistry
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Author Contributions
Rajjyoti Das – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Anupam Sarma – Conception and design, Drafting the article, Critical revision of the article, Final approval of the version to be published Partha Sarathi Chakraborty – Conception and design, Drafting the article, Critical revision of the article, Final approval of the version to be published Jagannath Dev Sharma – Conception and design, Drafting the article, Critical revision of the article, Final approval of the version to be published Amal Chandra Kataki – Conception and design, Critical revision of the article, Final approval of the version to be published |
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Guarantor of submission
The corresponding author is the guarantor of submission. |
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Source of support
None |
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Conflict of interest
Authors declare no conflict of interest. |
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Copyright
© Rajjyoti Das et al. 2014; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.) |
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About The Authors
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