Case Report
 
Noncompaction cardiomyopathy: A rare cardiomyopathy
Sachin Kumar Amruthlal Jain1, Brijesh Patel1, Timothy R Larsen1, Yousif Ismail1, Shukri David1
1MD, Providence Hospital and Medical Center, Southfield, MI.

doi:10.5348/ijcri-2013-09-358-CR-2

Address correspondence to:
Sachin Kumar Amruthlal Jain
MD, Department of Cardiology, Providence Hospital and Medical Centers
16001 W. Nine Mile Road
Southfield, MI
USA
Phone: 248 849 3968
Fax: 248 849 3151
Email: doctorsachin@gmail.com

Access full text article on other devices

  Access PDF of article on other devices

[HTML Full Text]   [PDF Full Text] [Print This Article]
[Similar article in Pumed] [Similar article in Google Scholar]


How to cite this article:
Jain SKA, Patel B, Larsen TR, Ismail Y, David S. Noncompaction cardiomyopathy: A rare cardiomyopathy. International Journal of Case Reports and Images 2013;4(9):467–470.


Abstract
Introduction: Noncompaction cardiomyopathy (NCCM) is a rare form of cardiomyopathy. The American Heart Association classified it as a genetic cardiomyopathy. The pathogenesis of this condition is attributed to the failure of trabecular myocardium to compact and underdeveloped microcoronary circulation.
Case Report: We present a case of a 72-year-old African American female who presented with shortness of breath and leg swelling and was found to have severe systolic dysfunction. Stress test showed ischemia. Left heart catheterization which included left ventriculogram showed prominent trabeculations suggestive of noncompaction cardiomyopathy.
Conclusion: This condition is often associated with other congenital cardiac defects and arrthymias. When it is present alone, it is called isolated noncompaction cardiomyopathy (INCCM). The treatment protocol for this cardiomyopathy is the same as other cardiomyopathies, and includes the management of arrhythmias, heart failure and potential risk of embolism.

Keywords: Noncompaction cardiomyopathy, Echocardiography, Heart failure, Congenital heart disease


[HTML Full Text]   [PDF Full Text]

Author Contributions
Sachin Kumar Amruthal Jain – Conception and design, Acquisition of data, Analysis and interpretation of data, Critical revision of the article, Final approval of the version to be published
Brijesh Patel – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published
Timothy Larsen – Acquisition of data, Analysis and interpretations, Critical revision of the article, Final approval of the version to be published
Yousif Ismail – Acquisition of data, Analysis and interpretations, Critical revision of the article, Final approval of the version to be published
Shukri David – Acquisition of data, Analysis and interpretations, Critical revision of the article, Final approval of the version to be published
Guarantor of submission
The corresponding author is the guarantor of submission.
Source of support
None
Conflict of interest
Authors declare no conflict of interest.
Copyright
© Sachin Kumar Amruthlal Jain et al. 2013; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.)