| Table of Contents |  |
|
Case Report
|
| Bilaterally symmetrical involvement in hirayama disease: A rare presentation |
| Anand Pai1, Umadevi V2, Suresh Saravanakumar3 |
|
1MBBS, Resident Doctor, Department of General Medicine, Aarupadai Veedu Medical College and Hospital, Pondicherry, India.
2MD, Professor, Department of General Medicine, Aarupadai Veedu Medical College and Hospital, Pondicherry, India. 3MD, Associate Professor, Department of General Medicine, Aarupadai Veedu Medical College and Hospital, Pondicherry, India. |
|
doi:10.5348/ijcri-2012-08-165-CR-12
|
|
Address correspondence to: Anand Pai Department of General Medicine Aarupadai Veedu Medical College and Hospital Kirumampakkam, Pondicherry- 607402 India Phone: Mob: +919841320712; Ph: 044-28342171 Email: cdrocks_87@yahoo.co.in |
|
[HTML Full Text]
[PDF Full Text]
|
| How to cite this article: |
| Pai A, Umadevi V, Saravanakumar S. Bilaterally symmetrical involvement in hirayama disease: A rare presentation. International Journal of Case Reports and Images 2012;3(8):43–45. |
|
Abstract
|
|
Introduction:
Hirayama disease (HD) or otherwise flexion cervical myelopathy is characterized by progressive muscular weakness and atrophy of the distal upper limbs most frequently seen in young males. Hirayama disease is thought to be secondary to an abnormal anterior displacement of the posterior dura with secondary compression of the lower cervical spinal cord and chronic injury to the anterior grey horn cells of cervical cord leading to localised cord atrophy. HD (brachial monomelic amyotrophy) is a unilateral or grossly asymmetric bilateral disease.
Case Report: A 26-year-old male who presented with progressive weakness and wasting in the distal muscles of both the upper limbs with no sensory involvement and autonomic involvement. Clinical, radiological and electrophysiologic findings in our patient were consistent with the diagnosis of HD. The patient was advised to wear a soft cervical collar. On three month follow up the patient had shown no progression of his disease. Conclusion: There are very sparse reports of bilaterally symmetric involvement and hence we report this case as bilateral symmetric is a severe form of the classic disease which remains undiagnosed due to a common notion that it is a unilateral or grossly asymmetric disease, hence we report this case. | |
|
Key Words:
Hirayama disease, Flexion cervical myelopathy, Bilateral symmetric involvement
| |
|
[HTML Full Text]
[PDF Full Text]
|
|
Author Contributions:
Anand Pai – Conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Critical revision of the article, Final approval of the version to be published Umadevi V – Conception and design, Analysis and interpretation of data, Critical revision of the article; Final approval of the version to be published Suresh Saravankumar – Analysis and interpretation of data, Critical revision of the article, Final approval of the version to be published |
|
Guarantor of submission:
The corresponding author is the guarantor of submission. |
|
Source of support:
None |
|
Conflict of interest:
Authors declare no conflict of interest. |
|
Copyright:
© Anand Pai et al. 2012; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.) |
|
|