Table of Contents    
Case Report
 
Ventriculo-peritoneal shunt blockage due to ruptured intracerebral dermoid cyst
Ahmad Abu-Omar1, Rupert Price2
1Specialty Registrar in ENT, Department of Otolaryngology, Crosshouse Hospital, Kilmarnock, UK.
2Consultant Neurosurgeon, Department of Neurosurgery, University Hospital of North Staffordshire, Stoke-on-Trent, UK.

doi:10.5348/ijcri-2011-09-53-CR-3

Address correspondence to:
Ahmad Abu-Omar
Department of Otolaryngology
Level 5, Crosshouse Hospital
Kilmarnock Road
Kilmarnock
KA2 0BE
United Kingdom
Phone: 00447792462582
Fax: 00441563827974
Email: aomar@doctors.org.uk

[HTML Full Text]   [PDF Full Text]

How to cite this article:
Abu-Omar A, Price R. Ventriculo-peritoneal shunt blockage due to ruptured intracerebral dermoid cyst. International Journal of Case Reports and Images 2011;2(9):9-12.


Abstract
Introduction: Intracranial dermoid cysts are rare congenital lesions that can rupture and disseminate intracranially. We present a unique case of a ruptured dermoid cyst leading to blockage of ventriculo-peritoneal shunts.
Case Report: A 19-year-old female presented with clumsiness, gait disturbance and occipital headache. Examination revealed an ataxic gait, positive Romberg’s sign, lateral gaze nystagmus and hyper-reflexia in all four limbs with bilateral positive Hoffman’s sign. A Magnetic Resonance scan revealed a large, heterogeneous midline cerebellar mass which had evidently ruptured at some point causing diffuse subarachnoid dissemination of fat. The patient underwent an uneventful posterior fossa craniectomy for removal of the cyst and was discharged home. She presented ten weeks later with headaches, ataxia, vomiting and decreased Glasgow Coma Scale. A cranial computed tomography (CT) scan showed ventriculomegaly which was treated with insertion of an external ventricular drain. The patient improved but attempts to clamp the external ventricular drain led to recurrence of symptoms. The patient underwent serial operations for ventriculo-peritoneal shunt insertion, but each time symptoms and Glasgow Coma Scale improved only temporarily. This was postulated to be due to free-floating intraventricular fat repeatedly clogging the shunts. Following its removal there has been no further symptomatic hydrocephalus. Endoscopic aspiration of the intraventricular lipoid material from the frontal horn before the final shunt revision.
Conclusion: Fat dissemination from ruptured intracranial dermoid cysts can lead to blockage of ventriculo-peritoneal shunts. We recommend the removal of intraventricular fat from the outset if cerebrospinal fluid diversion is required.

Key Words: Congenital, Dermoid cyst, Intracranial, Rupture

[HTML Full Text]   [PDF Full Text]

Author Contributions:
Ahmad Abu-Omar - Substantial contributions to conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Rupert Price - Substantial contributions to conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Guarantor of submission:
The corresponding author is the guarantor of submission.
Source of support:
None
Conflict of interest:
Authors declare no conflict of interest.
Copyright:
© Ahmad Abu-Omar et al. 2011; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.)