Case Report
 
Successful endoscopic third ventriculostomy after craniosynostosis reconstruction with cranial vault expansion after ventriculoperitoneal shunt failure
Smit Shah1, Rachana Tyagi2
1Rutgers Robert Wood Johnson Medical School, Medical Student Year 3, New Brunswick, New Jersey, USA
2Rutgers Robert Wood Johnson University Hospital, Pediatric Neurosurgeon, Department of Neurosurgery, New Brunswick, New Jersey, USA

Article ID: Z01201801CR10873SS
doi: 10.5348/ijcri-201804-CR-10873

Corresponding Author:
Smit Shah,
112 Montgomery Street,
Apt 3G, Highland Park,
New Jersey,
USA, 08904

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How to cite this article
Shah S, Tyagi R. Successful endoscopic third ventriculostomy after craniosynostosis reconstruction with cranial vault expansion after ventriculoperitoneal shunt failure. Int J Case Rep Images 2018;9(1):33–37.


ABSTRACT

Introduction: Syndromic craniosynostosis with growth restriction often causes increased intracranial pressure requiring shunting. Crouzon syndrome also known as branchial arch syndrome is an autosomal dominant disorder which has multiple phenotypic characteristics including proptosis, low set ears, bilateral strabismus, orofacial deformities affecting maxilla and mandible, and most importantly abnormal fusion of skull sutures also known as craniosynostosis.
Case Report: A 17-year-old male presented with severe Crouzon syndrome and brachycephaly who had a delayed cranial vault expansion. He subsequently developed intermittent shunt malfunction, which progressed to a complete obstruction. After successful endoscopic third ventriculostomy and return to baseline function the shunt was tied off.
Conclusion: Endoscopic third ventriculostomy (ETV) can be performed safely and effectively for shunt malfunction after cranial vault expansion in patients who may not have been candidates previously. By using ETV in addition to known traditional techniques of cranial vault expansion, patient’s prognosis and postoperative recovery can be expedited.

Keywords: Craniosynostosis, Crouzon syndrome, Expansion, Vault



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Author Contributions
Smit Shah – Substantial contributions to conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Rachana Tyagi – Substantial contributions to conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Guarantor of Submission
The corresponding author is the guarantor of submission.
Source of Support
None
Conflict of Interest
Authors declare no conflict of interest.
Copyright
© 2018 Smit Shah et al. This article is distributed under the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any medium provided the original author(s) and original publisher are properly credited. Please see the copyright policy on the journal website for more information.