Case Report
 
Orbital lymphangioma
Naser Salihu1, Anita Sylaj1
1Eye Clinic, University Clinical Center of Kosovo, Prishtina.

doi:10.5348/ijcri-2014-01-433-CR-6

Address correspondence to:
Naser Salihu
Dardania 6/9, No. 8, Sadik Zeneli
Prishtina, Postal code: 10000
Republic of Kosovo
Phone: +377 44 177 801
Email: nasersalihu@yahoo.com

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How to cite this article
Salihu N, Sylaj A. Orbital lymphangioma. International Journal of Case Reports and Images 2014;5(1):28–31


Abstract
Introduction: Orbital lymphangioma is a rare benign vascular malformation which may affect the conjunctiva, lids and orbit. Although hemodinamically isolated from the circulation, bleeding into the lumen may occur. Treatment options for orbital lymphangiomas include conservative management, partial surgical resection of the major cyst, needle aspiration, and intralesional injection of sclerosing agents and local radiotherapy. Recurrences in this disease are common because complete surgical excision is very difficult as the lesions are friable, not encapsulated, bleed easily and may infiltrate normal orbital structures.
Case Report: A 15-year-old boy presented in our institution with a sudden onset of pain proptosis, visual loss, restricted eye movement, diplopia and subconjunctival bleeding. Patient underwent complete ocular examination, clinical, echographic and radiological evaluation. Despite systemic steroid treatment during two weeks follow- up, situation was worsened. Signs of exposure keratopathy began to occur in cornea due to increased proptosis and intraocular pressure. Visual acuity continuously decreased because of decreased corneal transparency and presence of compressive optic neuropathy which were evident. As a result, we decided to perform orbital decompression. Subtotal excision of tumor and blood evacuation was performed. Pathological findings were suggestive of orbital lymphangioma. Postoperative course was uneventful.
Conclusion: Orbital lymphangioma has to be included in the differential diagnosis in any case of acute proptosis, especially in young patients. In cases which this condition causes retrobulbar hemorrhage with acute proptosis associated with exposure keratopathy, secondary glaucoma, compressive optic neuropathy and visual loss, orbital decompression is one of the choices of treatment to restore vision.

Keywords: Orbital lymphangioma, Retrobulbar hemorrhage, Acute proptosis, Orbital decompression


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Author Contributions
Naser Salihu – Substantial contributions to conception and design, Acquisition of data, Analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Anita Sylaj – Analysis and interpretation of data, Drafting the article, Revising it critically for important intellectual content, Final approval of the version to be published
Guarantor of submission
The corresponding author is the guarantor of submission.
Source of support
None
Conflict of interest
Authors declare no conflict of interest.
Copyright
© Naser Salihu et al. 2014; This article is distributed the terms of Creative Commons Attribution License which permits unrestricted use, distribution and reproduction in any means provided the original authors and original publisher are properly credited. (Please see Copyright Policy for more information.)



About The Authors

Naser Salihu is Assistant Professor in Medical Faculty and Chief of Department at University Eye Clinic in Prishtina, Kosovo. His research interests include orbital and eyelid surgery.